A Case of Adult Stills Disease: Not So Uncommon Cause of Fever of Unknown Origin
Arun Agarwal *
Department of Internal Medicine, Fortis Escorts Hospital, Jaipur, Rajasthan, India
Aakanksha Agarwal
Department of Radiodiagnosis, SMS Medical College, Jaipur, Rajasthan, India
Abu Saad Khan
Department of Internal Medicine, Fortis Escorts Hospital, Jaipur, Rajasthan, India
*Author to whom correspondence should be addressed.
Abstract
Adult still’s disease (ASD) is a defined clinical entity and a known cause of fever of unknown origin (FUO). It is a rare systemic inflammatory disorder characterized by a triad of symptoms: daily (quotidian) spiking fever (>39°C), arthritis and an evanescent salmon-colored rash. First described in 1971, it is a uncommon, difficult to diagnose, auto inflammatory, multisystem disorder. The disease is characterized by two subsets according to clinical and laboratory features: systemic or articular. Early diagnosis and treatment of the disease can prevent morbidity and mortality with a favorable outcome. We present and discuss a young male patient who presented as FUO and was diagnosed timely as ASD and treated with corticosteroids with a favorable prognosis.
Keywords: Auto inflammatory disease, adult onset stills disease, fever of unknown origin, Yamaguchi criteria, Fautrel criteria